ABSTRACT
The granulose cell tumor of the ovary is an uncommon cause of precocious puberty and only about 5% of these tumors occur in premenarchal girls. However 90% of them have the distinctive features of “Juvenile granulose cell tumor”. We report a case of a 2 ½ year old girl with pseudoprecocious puberty due to juvenile granulose cell tumor. Clinical features in this girl included bilateral breast enlargement, vaginal bleed-ing and a 7-cm-diameter mass in the lower abdomen. Investigations revealed advanced bone age, elevated level of serum estradiol with low levels of serum FSH and LH. A mixed solid and cystic mass at the right side of the ovaries was identified by an ultrasound examination. Right salpingo-oophorectomy was performed and histo-logical examination showed typical Juvenile granulose cell tumor.